Improved stable isotope dilution-gas chromatography-mass spectrometry method for serum or plasma free 3-hydroxy-fatty acids and its utility for the study of disorders of mitochondrial fatty acid beta-oxidation.
Jones PM, Quinn R, Fennessey PV, Tjoa S, Goodman SI, Fiore S, Burlina AB, Rinaldo P, Boriack, RL, Bennett MJ. Clinical Chemistry February 2000 46 149-55
Clinical applications of 3-hydroxy-fatty acid analysis by gas chromatography-mass spectrometry.
Jones PM, Bennett MJ BBA - Mol Cell Biol Lip 2011 1811 657-662
Mechanism of hyperinsulinism in short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency involves activation of glutamate dehydrogenase.
Li C, Chen P, Palladino A, Narayan S, Russell LK, Chen J, Stokes D, Butt YM, Jones PM, Collins HW, Strauss AW, Matschinsky FM, Bennett MJ, Stanley CA JBC 2010 41 285 31806-31818
Deorphanization of GPR109B as a receptor for the beta-oxidation intermediate 3-OH-octanoic acid and its role in the regulation of lipolysis
Ahmed K, Tunaru S, Langhans C-D, Hanson J, Michalski CW, Kolker S, Jones PM, Okun JG, Offermanns S. JBC 2009 33 284 21928-21933
Medium-chain fatty acids undergo elongation before β-oxidation in fibroblasts
Jones PM, Butt YM, Messmer B, Boriak, R, Bennett MJ Biochem Biophys Res Comm June 2006 346 193-197
Effects of odd-numbered medium-chain fatty acids on the accumulation of long-chain 3-hydroxy-fatty acids in long-chain L-3-hydroxyacyl CoA dehydrogenase (LCHAD) and mitochondrial trifunctional protein (MTFP) deficient skin fibroblasts.
Jones PM, Butt YM, Bennett MJ. Molecular Genetics and Metabolism 2004 81 (2) 96-99
Accumulation of 3-hydroxy-fatty acids in the culture medium of long-chain L-3-hydroxyacyl CoA dehydrogenase and mitochondrial trifunctional protein deficient skin fibroblasts: Implications for medium chain triglyceri
Jones PM, Butt Y, Bennett MJ. Pediatric Research May 2003 53(5) 783-7
The changing face of newborn screening: diagnosis of inborn errors of metabolism by tandem mass spectrometry.
Jones PM, Bennett MJ. Clinica Chimica Acta October 2002 324 121-8
Accumulation of free 3-hydroxy-fatty acids in the culture media of fibroblasts from patients deficient in long-chain 3-hydroxyacyl CoA dehydrogenase: a useful diagnostic aid.
Jones PM, Moffitt M, Joseph D, Harthcock PA, Boriack RL, Ibdah JA, Strauss AW, Bennett MJ. Clinical Chemistry July 2001 47(7) 1190-4